
Thermo Fisher Scientific alpha Galactosidase Polyclonal Antibody
Human alpha Galactosidase를 검출하는 Chicken Polyclonal Antibody. Western blot과 ELISA에 적합하며, 1:1,000–1:5,000 희석 사용. IgY fraction 정제, PBS buffer에 0.02% sodium azide 포함. 단기 4°C, 장기 -20°C 보관 권장.
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Applications
| Application | Tested Dilution | Publications |
|---|---|---|
| Western Blot (WB) | 1:1,000–1:5,000 | View 1 publication |
| ELISA | 1:1,000–1:5,000 | - |
Product Specifications
| 항목 | 내용 |
|---|---|
| Species Reactivity | Human |
| Published Species | Bacteria |
| Host / Isotype | Chicken / IgY |
| Class | Polyclonal |
| Type | Antibody |
| Immunogen | Mix of synthetic peptides corresponding to residues 55–64 and 396–407 of human alpha Galactosidase |
| Conjugate | Unconjugated |
| Form | Liquid |
| Concentration | 1 mg/mL |
| Purification | IgY fraction |
| Storage Buffer | PBS |
| Contains | 0.02% sodium azide |
| Storage Conditions | Store at 4°C short term. For long term storage, store at -20°C, avoiding freeze/thaw cycles. |
| Shipping Conditions | Ambient (domestic); Wet ice (international) |
| RRID | AB_2263438 |
Product Specific Information
- PA1-9528 detects Alpha Galactosidase in human samples.
- Suitable for Western blot and ELISA applications.
- Immunogen: mix of synthetic peptides corresponding to residues 55–64 and 396–407 of human alpha Galactosidase.
- Store at 4ºC for one week, and -20ºC for long term storage.
Target Information
This gene encodes a homodimeric glycoprotein that hydrolyzes the terminal alpha-galactosyl moieties from glycolipids and glycoproteins.
It predominantly hydrolyzes ceramide trihexoside and catalyzes the hydrolysis of melibiose into galactose and glucose.
Mutations in this gene cause Fabry disease, a lysosomal storage disorder resulting from a failure to catabolize alpha-D-galactosyl glycolipid moieties.
For Research Use Only. Not for use in diagnostic procedures. Not for resale without express authorization.
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