Thermo Fisher Scientific CLC-7 (CLCN7) Polyclonal Antibody

Thermo Fisher Scientific CLC-7 (CLCN7) Polyclonal Antibody

Applications

• Western Blot (WB)

Tested Dilution

• 1:200

Product Specifications

Product Specific Information

Reconstitution: 25 µL, 50 µL, or 0.2 mL double distilled water (DDW), depending on sample size.
The antibody ships as a lyophilized powder at room temperature. Upon arrival, store at -20°C.
Reconstituted solution can be stored at 4°C for up to 1 week. For longer storage, aliquot and keep at -20°C.
Avoid multiple freeze/thaw cycles. Centrifuge all antibody preparations before use (10000 × g, 5 min).

Target Information

The CLCN7 gene encodes chloride channel 7, a member of the CLC chloride channel family.
Chloride channels function in plasma membranes and intracellular organelles.
Defects in this gene cause osteopetrosis types OPTB4 (autosomal recessive) and OPTA2 (autosomal dominant, Albers-Schonberg disease).
Osteopetrosis is a rare genetic disorder characterized by abnormally dense bone due to defective resorption of immature bone.
OPTA2 is the most common form, typically appearing in adolescence or adulthood.

For Research Use Only. Not for use in diagnostic procedures. Not for resale without express authorization.

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