Thermo Fisher Scientific NAGA Monoclonal Antibody (OTI3A4), TrueMAB
인간 NAGA 단백질을 인식하는 마우스 단클론 항체로, Western blot 및 IHC(P)에서 사용 가능. Affinity chromatography로 정제된 액상 제품이며, 1 mg/mL 농도로 제공. PBS, BSA, 글리세롤 포함 완충액에 보관되며 -20°C에서 안정적.
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Applications and Tested Dilution
| Application | Tested Dilution |
|---|---|
| Western Blot (WB) | 1:500 |
| Immunohistochemistry (Paraffin) (IHC (P)) | 1:500 |
Product Specifications
| 항목 | 내용 |
|---|---|
| Species Reactivity | Human |
| Host / Isotype | Mouse / IgG1 |
| Class | Monoclonal |
| Type | Antibody |
| Clone | OTI3A4 |
| Immunogen | Full length human recombinant protein of human NAGA produced in HEK293T cell |
| Conjugate | Unconjugated |
| Form | Liquid |
| Concentration | 1 mg/mL |
| Purification | Affinity chromatography |
| Storage Buffer | PBS with 1% BSA, 50% glycerol |
| Contains | 0.02% sodium azide |
| Storage Conditions | -20°C, Avoid Freeze/Thaw Cycles |
| Shipping Conditions | Ambient (domestic); Wet ice (international) |
Target Information
NAGA (N-acetylgalactosaminidase, alpha), also known as alpha-galactosidase B or GALB, is a 411 amino acid lysosomal protein belonging to the glycosyl hydrolase 27 family. It functions as a homodimer and plays a critical role in glycolipid breakdown. The NAGA gene encodes a lysosomal enzyme that cleaves alpha-N-acetylgalactosaminyl groups from glycoconjugates and maps to human chromosome 22q13.2.
Defects in NAGA cause autosomal recessive disorders known as Schindler disease (types I, II, and III) or NAGA deficiency, characterized by varying degrees of neurologic manifestations.
- Type I: Most severe form
- Type II (Kanzaki disease): Mild intellectual impairment, angiokeratoma corporis diffusum
- Type III: Mild-to-moderate effects
For Research Use Only. Not for use in diagnostic procedures. Not for resale without express authorization.
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