Thermo Fisher Scientific CLCN7 Monoclonal Antibody (4A3)
CLCN7 단백질을 인식하는 Thermo Fisher Scientific의 Mouse Monoclonal Antibody (Clone 4A3). Western blot 및 ELISA에 적합하며, 인간 시료 반응성. 액상 형태로 제공되며, -20°C에서 보관. 연구용으로만 사용 가능.
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Applications
Western Blot (WB)
- Tested Dilution: 1:500–1:1,000
ELISA
- Tested Dilution: 1:500–1:1,000
Product Specifications
| 항목 | 내용 |
|---|---|
| Species Reactivity | Human |
| Host / Isotype | Mouse / IgG2a, kappa |
| Class | Monoclonal |
| Type | Antibody |
| Clone | 4A3 |
| Immunogen | CLCN7 (NP_001278, 706–805 a.a.) partial recombinant protein with GST tag (MW of GST tag alone: 26 kDa) |
| Conjugate | Unconjugated |
| Form | Liquid |
| Concentration | See Label |
| Storage Buffer | Ascites |
| Contains | No preservative |
| Storage Conditions | -20°C, Avoid Freeze/Thaw Cycles |
| Shipping Conditions | Ambient (domestic); Wet ice (international) |
Product Specific Information
Sequence of this protein is as follows:
LRLKDFRDAY PRFPPIQSIH VSQDERECTM DLSEFMNPSP YTVPQEASLP RVFKLFRALG LRHLVVVDNR NQVVGLVTRK DLARYRLGKR GLEELSLAQT
Target Information
The product of this gene belongs to the CLC chloride channel family of proteins. Chloride channels play important roles in the plasma membrane and in intracellular organelles. This gene encodes chloride channel 7 (CLCN7).
Defects in this gene are associated with:
- Osteopetrosis autosomal recessive type 4 (OPTB4), also known as infantile malignant osteopetrosis type 2
- Autosomal dominant osteopetrosis type 2 (OPTA2), also called Albers-Schonberg disease or marble disease
Osteopetrosis is a rare genetic disorder characterized by abnormally dense bone due to defective resorption of immature bone. OPTA2 is the most common form of osteopetrosis, typically occurring in adolescence or adulthood.
For Research Use Only.
Not for use in diagnostic procedures.
Not for resale without express authorization.
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