CacheBy
Thermo Fisher Scientific Dysferlin Recombinant Rabbit Monoclonal Antibody (ARC2178)
원본

Thermo Fisher Scientific Dysferlin Recombinant Rabbit Monoclonal Antibody (ARC2178)

상품 한눈에 보기

Recombinant rabbit monoclonal antibody targeting human Dysferlin (ARC2178). Western blot, IHC, ELISA에 적합하며, 높은 특이성과 재현성을 제공. 근위축증 관련 연구용으로 적합하며, -20°C에서 보관.

카탈로그번호
MA537920
판매단위
pk
카탈로그 보기

카탈로그

1개 옵션
회원가입 없이 바로 구매하세요
가입하지 않아도 비회원가로 구매하실 수 있습니다.
마지막 업데이트 2025. 08. 05. 오전 10:25
Thermo Fisher Scientific MA537920 Dysferlin Recombinant Rabbit Monoclonal Antibody (ARC2178) 100 ul pk판매 단위 pk ·
재고 확인 필요
699,900원VAT 포함 769,890원

Thermo Fisher Scientific · Thermo Fisher Scientific Dysferlin Recombinant Rabbit Monoclonal Antibody (ARC2178)

Applications and Tested Dilutions

Application Tested Dilution
Western Blot (WB) 1:500–1:2,000
Immunohistochemistry (Paraffin) (IHC (P)) 1:50–1:200
ELISA 1 µg/mL

Product Specifications

항목 내용
Species Reactivity Human
Host / Isotype Rabbit / IgG
Expression System HEK293 cells
Class Recombinant Monoclonal
Type Antibody
Clone ARC2178
Immunogen A synthetic peptide corresponding to amino acids 50–150 of human Dysferlin (Romeo) (UniProt ID: O75923)
Conjugate Unconjugated
Form Liquid
Concentration 0.8 mg/mL
Purification Affinity chromatography
Storage Buffer PBS, pH 7.3, with 50% glycerol, 0.05% BSA
Contains 0.02% sodium azide
Storage Conditions -20°C, Avoid Freeze/Thaw Cycles
Shipping Conditions Ambient (domestic); Wet ice (international)
RRID AB_2897840

Product Specific Information

  • Positive Samples: RD
  • Immunogen Sequence:
    FEWDLKGIPL DQGSELHVVV KDHETMGRNR FLGEAKVPLR EVLATPSLSA SFNAPLLDTK KQPTGASLVL QVSYTPLPGA VPLFPPPTPL EPSPTLPDLD V

Target Information

Dysferlin is the protein product of the 2p13 gene that is defective in patients with Limb-Girdle Muscular Dystrophy type 2B (LGMD2B) and Miyoshi Myopathy (MM). Dysferlin is normally localized to the muscle plasma membrane. In patients with LGMD2B and MM, immunoreactivity to dysferlin is severely reduced or lost, depending on the type of mutation. This antibody is used for the characterization of LGMD2B and MM.


For Research Use Only. Not for use in diagnostic procedures. Not for resale without express authorization.

Thermo Fisher Scientific 상품 둘러보기

전체보기

문의

0

아직 등록된 문의가 없어요.