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Thermo Fisher Scientific Mucolipin 1 Polyclonal Antibody
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Thermo Fisher Scientific Mucolipin 1 Polyclonal Antibody

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Human Mucolipin 1 단백질을 인식하는 goat polyclonal 항체로, WB 및 IHC에 사용 가능. 합성 펩타이드 항원을 기반으로 제작되었으며, 동결건조 형태로 제공. 연구용으로만 사용되며 장기 보관 시 -20°C 권장.

카탈로그번호
OSM00072W-100UL
판매단위
pk
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마지막 업데이트 2025. 08. 05. 오후 07:41
Thermo Fisher Scientific OSM00072W-100UL Mucolipin 1 Polyclonal Antibody 100 ul pk판매 단위 pk ·
재고 확인 필요
563,100원VAT 포함 619,410원

Thermo Fisher Scientific · Thermo Fisher Scientific Mucolipin 1 Polyclonal Antibody

Applications

Western Blot (WB)

  • Tested Dilution: 1:300–1:2,000

Immunohistochemistry (IHC)

  • Tested Dilution: 1:300–1:2,000

Miscellaneous PubMed (Misc)


Product Specifications

항목 내용
Species Reactivity Human
Published Species Not Applicable
Host / Isotype Goat / Ig
Class Polyclonal
Type Antibody
Immunogen A synthetic peptide from human Mucolipin 1 conjugated to blue carrier protein
Conjugate Unconjugated
Form Lyophilized
Concentration Not Determined
Storage Buffer Whole serum
Contains No preservative
Storage Conditions Store at 4°C short term. For long term storage, store at -20°C, avoiding freeze/thaw cycles. Glycerol (1:1) may be added for added stability.
Shipping Conditions Ambient (domestic); Wet ice (international)

Product Specific Information

  • Reconstitute in 100 µL of sterile water. Centrifuge to remove any insoluble material.
  • Specificity: Mucolipin 1, isoforms 1 and 2.

Target Information

Defects in Mucolipin-1 cause mucolipidosis type IV (MLIV), also known as sialolipidosis.
MLIV is an autosomal recessive lysosomal storage disorder characterized by:

  • Severe psychomotor retardation
  • Ophthalmologic abnormalities (corneal opacity, retinal degeneration, strabismus)
  • Storage bodies of lipids and water-soluble substances visible by electron microscopy
  • Most patients unable to speak or walk independently, developmental level of 1–2 years
  • Constitutive achlorhydria with secondary elevation of serum gastrin levels

For Research Use Only.
Not for use in diagnostic procedures.
Not for resale without express authorization.

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