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Thermo Fisher Scientific Mucolipin 1 Polyclonal Antibody
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Human Mucolipin 1 단백질을 인식하는 goat polyclonal 항체로, WB 및 IHC에 사용 가능. 합성 펩타이드 항원을 기반으로 제작되었으며, 동결건조 형태로 제공. 연구용으로만 사용되며 장기 보관 시 -20°C 권장.
- 카탈로그번호
- OSM00072W-100UL
- 판매단위
- pk
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마지막 업데이트 2025. 08. 05. 오후 07:41
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Thermo Fisher Scientific OSM00072W-100UL Mucolipin 1 Polyclonal Antibody 100 ul pk판매 단위 pk ·
재고 확인 필요
563,100원VAT 포함 619,410원
Thermo Fisher Scientific · Thermo Fisher Scientific Mucolipin 1 Polyclonal Antibody
Applications
Western Blot (WB)
- Tested Dilution: 1:300–1:2,000
Immunohistochemistry (IHC)
- Tested Dilution: 1:300–1:2,000
Miscellaneous PubMed (Misc)
- Publications: View 1 publication
Product Specifications
| 항목 | 내용 |
|---|---|
| Species Reactivity | Human |
| Published Species | Not Applicable |
| Host / Isotype | Goat / Ig |
| Class | Polyclonal |
| Type | Antibody |
| Immunogen | A synthetic peptide from human Mucolipin 1 conjugated to blue carrier protein |
| Conjugate | Unconjugated |
| Form | Lyophilized |
| Concentration | Not Determined |
| Storage Buffer | Whole serum |
| Contains | No preservative |
| Storage Conditions | Store at 4°C short term. For long term storage, store at -20°C, avoiding freeze/thaw cycles. Glycerol (1:1) may be added for added stability. |
| Shipping Conditions | Ambient (domestic); Wet ice (international) |
Product Specific Information
- Reconstitute in 100 µL of sterile water. Centrifuge to remove any insoluble material.
- Specificity: Mucolipin 1, isoforms 1 and 2.
Target Information
Defects in Mucolipin-1 cause mucolipidosis type IV (MLIV), also known as sialolipidosis.
MLIV is an autosomal recessive lysosomal storage disorder characterized by:
- Severe psychomotor retardation
- Ophthalmologic abnormalities (corneal opacity, retinal degeneration, strabismus)
- Storage bodies of lipids and water-soluble substances visible by electron microscopy
- Most patients unable to speak or walk independently, developmental level of 1–2 years
- Constitutive achlorhydria with secondary elevation of serum gastrin levels
For Research Use Only.
Not for use in diagnostic procedures.
Not for resale without express authorization.
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