Thermo Fisher Scientific CPS1 Recombinant Rabbit Monoclonal Antibody (JB40-33)

Thermo Fisher Scientific CPS1 Recombinant Rabbit Monoclonal Antibody (JB40-33)

Applications and Tested Dilutions

• Western Blot (WB): 1:500–1:1,000
• Immunohistochemistry (Paraffin) [IHC (P)]: 1:50–1:200
• Immunocytochemistry (ICC/IF): 1:50–1:200

Product Specifications

Product Specific Information

Positive Control: HepG2, SiHa, human liver tissue, mouse small intestine tissue.

Target Information

The mitochondrial enzyme encoded by this gene catalyzes synthesis of carbamoyl phosphate from ammonia and bicarbonate. This reaction is the first committed step of the urea cycle, important for removal of excess urea from cells. The encoded protein may also represent a core mitochondrial nucleoid protein. Three transcript variants encoding different isoforms have been identified for this gene. The shortest isoform may not be localized to the mitochondrion. Mutations in this gene are associated with carbamoyl phosphate synthetase deficiency, susceptibility to persistent pulmonary hypertension, and venoocclusive disease after bone marrow transplantation.

For Research Use Only. Not for use in diagnostic procedures. Not for resale without express authorization.

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