
Thermo Fisher Scientific NAGLU Monoclonal Antibody (1B7)
NAGLU 단백질을 인식하는 Mouse IgG2a monoclonal antibody (Clone 1B7). Western blot 및 ELISA에 최적화. 인간 및 생쥐 반응성. PBS buffer, 무보존제, -20°C 보관. 연구용 전용.
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Applications
Western Blot (WB)
- Tested Dilution: 1–5 µg/mL
ELISA
- Tested Dilution: 10 µg/mL
Product Specifications
| 항목 | 내용 |
|---|---|
| Species Reactivity | Human, Mouse |
| Host / Isotype | Mouse / IgG2a, kappa |
| Class | Monoclonal |
| Type | Antibody |
| Clone | 1B7 |
| Immunogen | NAGLU (NP_000254, 644–742 a.a.) partial recombinant protein with GST tag (GST tag MW: 26 kDa) |
| Conjugate | Unconjugated |
| Form | Liquid |
| Concentration | See Label |
| Purification | Affinity chromatography |
| Storage Buffer | PBS, pH 7.4 |
| Contains | No preservative |
| Storage Conditions | -20°C, Avoid Freeze/Thaw Cycles |
| Shipping Conditions | Ambient (domestic); Wet ice (international) |
Product Specific Information
Sequence of this protein is as follows:
YQLTLWGPEG NILDYANKQL AGLVANYYTP RWRLFLEALV DSVAQGIPFQ QHQFDKNVFQ LEQAFVLSKQ RYPSQPRGDT VDLAKKIFLK YYPGWVAGS
Target Information
This gene encodes an enzyme that degrades heparan sulfate by hydrolysis of terminal N-acetyl-D-glucosamine residues in N-acetyl-alpha-D-glucosaminides.
Defects in this gene are the cause of mucopolysaccharidosis type IIIB (MPS-IIIB), also known as Sanfilippo syndrome B.
This disease is characterized by lysosomal accumulation and urinary excretion of heparan sulfate.
For Research Use Only. Not for use in diagnostic procedures. Not for resale without express authorization.
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