Thermo Fisher Scientific alpha Galactosidase Monoclonal Antibody (B1)
Thermo Fisher Scientific의 alpha Galactosidase Monoclonal Antibody (B1)는 인간 단백질을 인식하는 Mouse IgG2b 항체입니다. Western blot과 IHC(P)에서 사용 가능하며, 고순도 Protein A/G 정제 형식으로 제공됩니다. 액상 형태로 -20°C 보관, 연구용으로 적합합니다.
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Applications
Western Blot (WB)
- Tested Dilution: 0.5–2 µg/mL
Immunohistochemistry (Paraffin) (IHC (P))
- Tested Dilution: 5–20 µg/mL
Product Specifications
| 항목 | 내용 |
|---|---|
| Species Reactivity | Human |
| Host / Isotype | Mouse / IgG2b, kappa |
| Class | Monoclonal |
| Type | Antibody |
| Clone | B1 |
| Immunogen | Recombinant protein Galactosidase Alpha (aa 81–429 of target protein) |
| Conjugate | Unconjugated |
| Form | Liquid |
| Concentration | 1 mg/mL |
| Purification | Protein A/G |
| Storage buffer | PBS with 50% glycerol |
| Contains | 0.05% ProClin 300 |
| Storage conditions | -20°C |
| Shipping conditions | Wet ice |
| RRID | AB_2899072 |
Target Information
This gene encodes a homodimeric glycoprotein that hydrolyzes terminal alpha-galactosyl moieties from glycolipids and glycoproteins. The enzyme primarily hydrolyzes ceramide trihexoside and catalyzes the hydrolysis of melibiose into galactose and glucose. Mutations in this gene can impair enzyme synthesis, processing, and stability, leading to Fabry disease—a rare lysosomal storage disorder resulting from defective catabolism of alpha-D-galactosyl glycolipid moieties.
For Research Use Only. Not for use in diagnostic procedures. Not for resale without express authorization.
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